A Case of Erdheim-Chester Disease with periodic fever and knee pain.
- Author:
Jong Rak HONG
1
;
Hong Ghi LEE
;
Young Hyeh KO
;
Joong Mo AHN
;
Yeon Hyeon CHOI
;
Byung Tae KIM
Author Information
1. Department of Medicine, Samsung Medical Center Sungkyunkwan University, College of Medicine, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Erdheim-Chester disease(ECD);
Langerhans cell histiocytosis(LCH);
foamy histiocyte
- MeSH:
Erdheim-Chester Disease*;
Fever*;
Histiocytes;
Histiocytosis;
Knee*;
Korea;
Lipidoses;
Myalgia
- From:Korean Journal of Medicine
1999;56(4):542-546
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
ECD is a rare, non-Langerhans form of histiocytosis. The first case was reported in 1930 by Chester and the term ECD was first described by Jaffe in 1972. Many authors have suggested that ECD is a part of the spectrum of Langerhans cell histiocytosis(LCH), whereas others believe ECD as a distinct lipoidosis because of the symmetric distribution of the long bone lesions on the roentgenogram and the lack of Langerhans granules and S-100 antibody staining in the foamy histiocytes. We experienced a case of Erdheim-Chester disease (ECD) with periodic night fever, myalgia and both knee pain, the first case reported in Korea.
