Surgical treatment of Supravalvular Aortic Stenosis.
- Author:
Woo Ik CANG
1
;
Sam Se OH
;
Jeong Ryul LEE
;
Yong Jin KIM
;
Joon Rhyang RHO
;
Kyung Phill SUH
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Seoul National University College of Medicine, Korea.
- Publication Type:Original Article
- Keywords:
Aortic stenosis;
supravalvular
- MeSH:
Angioplasty;
Aorta;
Aortic Stenosis, Supravalvular*;
Aortic Valve Insufficiency;
Aortic Valve Stenosis;
Cardiac Catheterization;
Cardiac Catheters;
Child;
Echocardiography;
Glass;
Hemodynamics;
Humans;
Male;
Mortality;
Pulmonary Valve Stenosis;
Williams Syndrome
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
1998;31(8):763-769
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
BACKGROUND: Supravalvular aortic stenosis is a rare form of congenital cardiac anomaly involving ascending aorta distal to coronary orifice. MATERIALS AND METHODS: We operated 12 cases of supravalvular aortic stenosis between July 1986 and March 1997. Age ranged from 4 to 17 (mean 10.2) years and 11 of them were male. Nine patients had clinical features of Williams syndrome. We experienced two types of supravalvular aortic stenosis, including 10 hour glass type and 2 diffuse type. RESULTS: Preoperative transaortic pressure gradient ranged from 40 to 180 (mean 92) mmHg by cardiac catheterization. Pulmonary stenosis was associated in 5 and 2 of them required angioplasty. Operative techniques included 6 standard aortoplasty with elliptical patch, 4 extended aortoplasty with inverted Y shaped patch, and 2 modified Brom's repair. There were no operative deaths. Postoperative echocardiographic evaluation was done at a mean interval of 12 months. Grade I or II aortic regurgitation was found in 3 cases. Postoperative cardiac catheterization revealed a mean transaortic pressure gradient of 26 (range 0 to 75) mmHg. A mean pressure drop was 78 (range 30 to 114) mmHg. All patients were followed up for a mean of 40 (range 1 to 67) months with uneventful clinical course. CONCLUSIONS: Our data proved the low mortality and excellent hemodynamic improvement after surgical relief of supravalvular aortic stenosis in children.
