Asplenia(right atrial isomerism) diagnosed by prenatal ultrasonography: Report of One Case.
- Author:
Jung Eun YEON
;
Yong Gyun YOO
;
Eun Joo KANG
;
Hea Kyoung HUR
;
Dong Hee PARK
;
Kyoung Seo KIM
;
Sook Hee HONG
;
Hwa Sook MOON
- Publication Type:Case Report
- Keywords:
Asplenia;
prenatal ultrasonography
- MeSH:
Heart Defects, Congenital;
Heterotaxy Syndrome;
Isomerism;
Pulmonary Atresia;
Scimitar Syndrome;
Transposition of Great Vessels;
Ultrasonography, Prenatal*
- From:Korean Journal of Obstetrics and Gynecology
1999;42(9):2084-2087
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The syndromes of left atrial isomerism and right atrial isomerism, called polysplenia and asplenia syndromes, respectively, consist of congenital heart defects with disturbances in normal left right isometry, and the etiology of atrial isomerism remains unclear. Right atrial isomerism is traditionally associated with severe cardiac defects, especially complete atrioventricular septal defect, transposition of great arteries, pulmonary atresia, and total anomalous pulmonary venous return. Recently, we encountered one case of asplenia diagnosed by prenatal ultrasonography. We report a case with brief review of the literatures.
