A case of Maffucci's syndrome.
- Author:
Jin Hyoung WON
;
Won HUR
;
Enug Ho CHOI
;
Seung Kyung HANN
- Publication Type:Original Article
- Keywords:
Maffuccis Syndrorne;
Enchondroma;
Hemangioma
- MeSH:
Child;
Chondroma;
Chondromatosis;
Enchondromatosis;
Female;
Hemangioma;
Humans;
Incidence;
Mesoderm
- From:Korean Journal of Dermatology
1993;31(4):616-619
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Maffucci's syndrome is a congenital, non-hereditary mesodermal d splasia manifested by multiple enchondromas and hemangiomas. Several case reports and reviews indicate that there is a tendency toward malignant transformation of the enchondroma. The incidence of malignancy may be as high as 30%. We report a case of 10-year-old female with multiple hemangiomas on the face, palms, and soles and skeletal chondromatoses of the multiple bones.
