A Case of Pityriasis Rubra Pilaris in an Infant.
- Author:
Tae Gyun LIM
1
;
Sung Joo LEE
;
Young Keun KIM
;
Gwang Seong CHOI
Author Information
1. Department of Dermatology, College of Medicine, Inha University, Incheon, Korea. garden@inha.ac.kr
- Publication Type:Case Report
- Keywords:
Pityriasis rubra pilaris;
Infant
- MeSH:
Citrus sinensis;
Classification;
Dermis;
Diagnosis;
Epidermis;
Erythema;
Humans;
Infant*;
Keratoderma, Palmoplantar;
Male;
Parakeratosis;
Phototherapy;
Pityriasis Rubra Pilaris*;
Pityriasis*
- From:Korean Journal of Dermatology
2002;40(1):92-94
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Pityriasis rubra pilaris is a rare papulosquamous and keratotic disease. The orange hue to the erythema, the thickening of the palms and soles and so called 'islands of normal skin' contribute to establish the diagnosis based on morphologic features. We present a 6-month-old male patient with multiple scaly erythematous patches and 'island of normal skin' on the face. There is no palmoplantar keratoderma, nor onychopathy. Histopathologic findings revealed alternating parakeratosis and hypergranulosis in the epidermis and mild perivascular lymphocytic infiltration in the dermis. Unlike to Griffiths classification, he showed good responses to topical steroid and UV phototherapy.
