Anesthetic Management of Myotonic Dystrophy: A case report.
10.4097/kjae.2003.44.3.414
- Author:
Byung Hee LEE
1
;
Jong Yeon LEE
;
Chung Hyun PARK
;
Min Ku KIM
;
Heon Rak LEE
Author Information
1. Department of Anesthesiology, College of Medicine, University of Pochon CHA, Sungnam, Korea. lbhaak@hanmail.net
- Publication Type:Case Report
- Keywords:
Anesthetic management;
myotonic dystrophy
- MeSH:
Analgesia;
Anesthesia;
Electric Stimulation;
Humans;
Hypothermia;
Hysterectomy;
Muscular Diseases;
Myotonia;
Myotonic Dystrophy*;
Shivering
- From:Korean Journal of Anesthesiology
2003;44(3):414-417
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Myotonic dystrophy is a muscle disorder characterized by progressive muscle wasting and weakness associated with myotonia. It is a systemic disease transmitted in an autosomal dominant pattern. Myotonia may be precipitated by hypothermia, shivering, and mechanical or electrical stimulation. Furthermore, sensitivity to sedative, anesthetic and neuromusclular blocking agents may result in intraoperative and early postoperative cardiovascular and respiratory complications, as well as prolonged recovery from anesthesia. Therefore, a patient with myotonic dystrophy is at high risk for complications from anesthetic management. We report the successful anesthetic management of such a patient undergoing a total abdominal hysterectomy, in which we used an epidural technique for intraoperative anesthesia and postoperative analgesia.
