Ruptured Tricuspid Valve Papillary Muscle in a Neonate with Intractable Persistent Fetal Circulation.
10.4070/kcj.2015.45.4.340
- Author:
Ja Kyoung YOON
1
;
Hye Rim KIM
;
Hye Won KWON
;
Bo Sang KWON
;
Gi Beom KIM
;
Eun Jung BAE
;
Chung Il NOH
;
Woong Han KIM
Author Information
1. Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea. eunjbaek@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Cyanosis;
Neonate;
Tricuspid regurgitation;
Papillary muscles;
Cardiac surgery
- MeSH:
Anoxia;
Cardiac Output, Low;
Cyanosis;
Diagnosis;
Extracorporeal Membrane Oxygenation;
Female;
Humans;
Infant, Newborn*;
Male;
Nitric Oxide;
Papillary Muscles*;
Parturition;
Perinatal Mortality;
Persistent Fetal Circulation Syndrome*;
Prolapse;
Rupture;
Thoracic Surgery;
Tricuspid Valve Insufficiency;
Tricuspid Valve*;
Vascular Resistance
- From:Korean Circulation Journal
2015;45(4):340-343
- CountryRepublic of Korea
- Language:English
-
Abstract:
Unguarded tricuspid regurgitation (TR) due to a flail tricuspid leaflet is a rare condition of newborn cyanosis. A high perinatal mortality has been associated with this fatal condition. But, there are feasible surgical repairs to improve survival. We report the case of a male full-term neonate with intractable hypoxia. He had profound tricuspid insufficiency and leaflet prolapse caused by a ruptured papillary muscle supporting the anterior leaflet of the tricuspid valve. He presented with severe cyanosis and respiratory distress immediately after birth. Despite medical management, the pulmonary vascular resistance was not decreased and a low cardiac output persisted. Initial stabilization was accomplished with nitric oxide and extracorporeal membrane oxygenation. The tricuspid valve repair surgery was successfully performed subsequently. TR resulting from papillary muscle rupture is a potentially lethal condition. Timely diagnosis and proper surgical treatment can be lifesaving.
