Aggressive Surgical Treatment for Complex Cardiac Anomalies Associated with Right Atrial Isomerism.
- Author:
Ui Dong HWANG
1
;
Tae Jin YUN
;
Sung Ho JUNG
;
Won Kyoung JHANG
;
Young Hwue KIM
Author Information
1. Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine, Korea. tjyun@amc.seoul.kr
- Publication Type:Case Report
- Keywords:
Heterotaxy;
Pulmonary vein, total anomalous return;
Pulmonary artery, collateral;
Extracorporeal membrane oxygenation
- MeSH:
Arteries;
Drainage;
Echocardiography;
Extracorporeal Membrane Oxygenation;
Female;
Heterotaxy Syndrome*;
Humans;
Hyperemia;
Infant;
Intubation, Intratracheal;
Oxygen;
Oxygenators;
Oxygenators, Membrane;
Scimitar Syndrome;
Tracheal Stenosis;
Tracheostomy
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2007;40(8):569-573
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A 3 month old female baby, who had been diagnosed with right atrial isomerism associated with total anomalous pulmonary venous return (TAPVR), a functional single ventricle and major aortopulmonary collateral arteries (MAPCA), underwent left MAPCA unifocalization and left Blalock-Taussig shunt (3.5 mm) at 3 months of age. The postoperative course was complicated by pulmonary venous congestion, and the drainage site of the TAPVR was found to be stenotic on echocardiography. We performed sutureless repair of the TAPVR along with unifocalization of the right MAPCA. She was put on an extracorporeal membrane oxygenator for 8 days after the 2nd operation, and she was able to come off the oxygenator with the placement of a central shunt (3 mm). She developed tracheal stenosis, which was presumably due to longstanding endotracheal intubation, and she then underwent tracheostomy. She was discharged to home on day 104 after the 1st operation, and she has been followed up for 2 months in a good clinical condition.
