A Case of Klippel-Trenaunay-Weber Syndrome with Sigmoid Varices.
- Author:
Yong Woo CHUNG
1
;
Dong Soo HAN
;
Chang Hee PAIK
;
Yoon Kyung PARK
;
Jong Pyo KIM
;
Hang Lak LEE
;
Jin Bae KIM
;
Joo Hyun SOHN
;
Joon Soo HAHM
;
Hwon Kyum PARK
Author Information
1. Department of Medicine, Hanyang University Kuri Hospital, Kuri, Korea. hands@hanyang.ac.kr
- Publication Type:Case Report
- Keywords:
Klippel-Trenaunay-Weber syndrome;
Sigmoid varices;
Vena cava occlusion
- MeSH:
Adult;
Colon;
Colon, Sigmoid*;
Esophageal and Gastric Varices;
Female;
Hemangioma;
Hemorrhage;
Humans;
Hypertrophy;
Klippel-Trenaunay-Weber Syndrome*;
Varicose Veins*;
Vascular Malformations;
Vena Cava, Inferior
- From:Korean Journal of Gastrointestinal Endoscopy
2003;27(1):21-25
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Colonic varix, which is a rare cause of lower gastrointestinal bleeding, can be developed by various diseases. Colonic variceal bleeding is more fatal than esophageal variceal bleeding. Klippel-Trenaunay-Weber syndrome is a rare congenital vascular malformation characterized by the clinical triad of bony or soft tissue hypertrophy, hemangioma and varicosities or vascular malformations. We report a 42-year-old female patient with fatal sigmoid variceal bleeding. She had dilated vessels over her body and face, and both superior and inferior vena cava were obstructed. She underwent an emergent operation due to uncontrolled massive bleeding from sigmoid varices. We report a case of Klippel-Trenaunay-Weber syndrome with literature review.