Anesthetic Experience for Freeman-Sheldon Syndrome: A case report.
10.4097/kjae.1999.36.1.158
- Author:
Jun Heum YON
1
;
Seung Jun LEE
;
Tae Ho OH
;
Ji Young SON
Author Information
1. Department of Anesthesiology, Sangge Paik Hospital, College of Medicine, Inje University, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Anesthetic technique, total intravenous anesthesia;
Genetic factors, Freeman-Sheldon syndrome;
Monitoring, somatosensory evoked potential
- MeSH:
Bronchoscopy;
Child;
Evoked Potentials, Somatosensory;
Female;
Fentanyl;
Fingers;
Humans;
Intubation;
Lip;
Microstomia;
Muscular Diseases;
Operating Rooms;
Palate;
Propofol
- From:Korean Journal of Anesthesiology
1999;36(1):158-161
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Freeman-Sheldon syndrome is a rare congenital myopathy principally characterized by facial and skeletal abnormalities. We report a case of a Freeman-Sheldon syndrome in 12-year-old girl correction of undergoing kyphoscoliosis under somatosensory evoked potential monitoring. She had a characteristic appearance of Freeman-Sheldon syndrome such as hypoplastic alae nasi, high narrow palate, marked microstomia with pursed lips and clenched fingers. On arriving at the operating room, she was intubated by awake nasotracheal intubation with fiberoptic bronchoscopy and anesthetized with propofol and fentanyl.
