Epidermolysis Bullosa Dystrophica Associated with Multiple Esophageal Strictures: A Case Report.
10.3348/jkrs.1998.38.2.297
- Author:
Kyung Seung OH
1
;
Sung Tack CHOI
;
Gyoo Sik JUNG
;
Jin Do HUH
;
Ki Seok SUH
;
Young Duk JOH
Author Information
1. Department of Diagnostic Radiology, Gospel Hospital, Medical College of Kosin University.
- Publication Type:Case Report
- Keywords:
Skin, abnormalities;
Esophagus, stenosis abstruction
- MeSH:
Congenital Abnormalities;
Constriction, Pathologic*;
Deglutition Disorders;
Epidermolysis Bullosa Dystrophica*;
Epidermolysis Bullosa*;
Esophagus;
Extremities;
Mucous Membrane;
Skin;
Skin Diseases;
Ulcer
- From:Journal of the Korean Radiological Society
1998;38(2):297-299
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Epidermolysis bullosa dystrophica is a rare skin disease characterized by milia, nail dystrophy, andblistering of the skin and mucous membranes in response to minimal trauma. A forty years old man had typical skinlesions on the extremities, and the presence of distal phalangeal wedge deformity with soft tissue webbing wasnoted. multiple segmental strictures and ulceration involved the cervical and distal esophagus. Esophageal balloondilatation was therefore performed and dysphagia was relieved. The authors describe a case involving multipleesophageal strictures and musculoskeletal lesion, with clinically and radiologically documented epidermolysisbullosa dystrophica.
