A Case of Sirenomelia without Oligohydramnios Diagnosed in Early Second Trimester.
- Author:
Hyun Ju PARK
1
;
Hyun Sook AN
;
Jo Eun KIM
;
Seung A LEE
;
Kyoung A CHOI
;
Sun Ji JEONG
;
Won Young CHI
Author Information
1. Department of Obstetrics and Gynecology, Ilsin Christian Hospital, Busan, Korea. banana3592@hanmail.net
- Publication Type:Case Report
- Keywords:
Sirenomelia;
Oligohydramnios;
Renal agenesis
- MeSH:
Abortion, Therapeutic;
Early Diagnosis;
Ectromelia*;
Female;
Humans;
Incidence;
Oligohydramnios*;
Parturition;
Pregnancy;
Pregnancy Trimester, Second*;
Prognosis;
Single Umbilical Artery;
Ureter;
Urinary Bladder;
Urogenital System
- From:Korean Journal of Perinatology
2006;17(1):94-98
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Sirenomelia is rare congenital malformation characterized by fusion of the lower extrimities associated anomalies included absence of urogenital system (bilateral renal agenesis, absent ureter, urinary bladder, absent internal and external genitalia), induced severe oligohydramnios, anorectal atresia, single umbilical artery, pulmonary hypoplasia. The incidence is 1:60000 births. Survival is extremely rare, and only possible, in the absence of bilateral renal agenesis. In view of the dismal prognosis, early diagnosis allows for earlier and less traumatic therapeutic abortion. We report a case of sirenomelia without oligohydramnios diagnosed in early second trimester.
