A case of allgrove syndrome.
- Author:
Han Sul LEE
1
;
Sang Min YUM
;
Dong Chae LEE
;
Byung Hoon KIM
;
Jong Hyo LEE
;
Sung Hyun LEE
;
Dae Sik KIM
;
Kun Hyung KIM
;
Soon Hee PARK
Author Information
1. Department of Internal Medicine, Mokpo Catholic Hospital, Mokpo, Korea. daha@netian.com
- Publication Type:Case Report
- Keywords:
Glucocorticoids;
Achalasia;
Esophageal
- MeSH:
Adolescent;
Adrenal Insufficiency;
Esophageal Achalasia;
Esophagus;
Glucocorticoids;
Humans;
Korea;
Male;
Parturition
- From:Korean Journal of Medicine
2002;62(5):537-542
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Allgrove syndrome, also known as Tripple A syndrome is characterized by ACTH-resistant adrenal insufficiency, achalasia of esophagus and alacrima. Since its first description by Allgrove et al. (1978), more than 60 cases from all over the world have been reported. In Korea, however, there was no report of this Allgrove syndrome. We report studies on a 18-year old male patient with this rare triad. The patient had alacrima from birth; isolated glucocorticoids deficiency had been diagnosed at 6 years of age and achalasia at age 18. We report the case with the review of literature.
