Atypical Vogt-Koyanagi-Harada Syndrome in a 7-Year-Old Boy.
- Author:
Jaeryung OH
1
;
In Kyung OH
;
Kuhl HUH
Author Information
1. Department of Ophthalmology, Korea University College of Medicine, Korea. dumky@unitel.co.kr
- Publication Type:Case Report
- Keywords:
Children;
Vogt-Koyanagi-Harada syndrome;
White dot syndrome
- MeSH:
Adrenal Cortex Hormones;
Adult;
Alopecia;
Child*;
Hair;
HLA-DR4 Antigen;
Humans;
Inflammation;
Leukocytes;
Male*;
Optic Nerve Diseases;
Retina;
Retinal Detachment;
Retinaldehyde;
Telescopes;
Uveitis, Anterior;
Uveomeningoencephalitic Syndrome*;
Visual Acuity
- From:Journal of the Korean Ophthalmological Society
2003;44(9):2184-2190
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
PURPOSE: Vogt-Koyanagi-Harada syndrome is more common in adults than in children. We report a atypical case of Vogt-Koyanagi-Harada syndrome like white dot syndromes in a 7-year-old child. METHODS: A 7-year-old child visited with complaints of decreased binocular visual acuity. Under ophthalmologic examination, anterior uveitis and optic neuropathy were found. But there was no other retinal lesion. After high-dose intravenous corticosteroids pulse therapy, yellow pigment lesions like white dot syndromes developed in peripheral retina and enlarged without serous retinal detachment. RESULTS: In 5 months after high-dose intravenous corticosteroids pulse therapy, anterior inflammation was decreased and visual acuity was 0.8 in both eyes. But depigmented retinal lesions were increased and sunset glow occurred. Alopecia and poliosis of hair were found. Human leukocyte antigen typings revealed HLA-DR4 antigen.