A Case Of Di Guglielmo Syndrome.
- Author:
In Soon PARK
1
;
Choong Rae KIM
;
Jae Seon PARK
;
Young Jeon KIM
Author Information
1. Dept. of Pediatrics, Pusan Gospel Hospital, Korea.
- Publication Type:Original Article
- MeSH:
Adolescent;
Bone Marrow;
Dizziness;
Female;
Granulocyte Precursor Cells;
Humans;
Myeloid Cells;
Nose;
Rare Diseases
- From:Journal of the Korean Pediatric Society
1980;23(10):843-848
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We have experienced a case of Di Guglielmo Syndrome in a 15 years old girl who had the cheif complaints of dizziness, gereral malaise and fine pustules around the nose. It is a systemic hemopathy characterized by abnormal proliferation of defective erythroid and myeloid cells and is a rare disease in childhood. The peripheral blood showed many rubriblasts, myeloblasts, metamyelocytes and bone marrow also showed atypical prorubricytes and bizzar multinucleated rubriblasts. Brief review of related literatures was made.
