Aortic Root Replacement in Patient of Right Ventricular Hypoplasia with Annuloaortic Ectasia, Ventricular Septal Defect and Aortic Regurgitation: Report of 1 case.
- Author:
Man Jong BAEK
1
;
Chan Young NA
;
Sam Se OH
;
Woong Han KIM
;
Sung Wook WHANG
;
Cheol LEE
;
Yunhee CHANG
;
Won Min JO
;
Jae Hyun KIM
;
Hong Ju SEO
;
Sang Soo KANG
;
Hyun Soo MOON
;
Young Kwan PARK
;
Chong Whan KIM
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Sejong Heart Institute, Korea. koreaheartsurgeon@hotmail.com
- Publication Type:Case Report
- MeSH:
Aortic Valve Insufficiency*;
Cardiac Catheterization;
Cardiac Catheters;
Cardiopulmonary Bypass;
Dilatation, Pathologic*;
Heart Septal Defects, Ventricular*;
Heart Ventricles;
Humans;
Male;
Replantation;
Transplants;
Tricuspid Valve;
Weaning;
Young Adult
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2003;36(7):510-513
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Annuloaortic ectasia, aortic regurgitation (AR), and ventricular septal defect (VSD) in patients with right ventricular hypoplasia is a very rare condition. We report a patient who underwent aortic root replacement with a composite graft for annuloaortic ectasia associated with VSD and AR in right ventricular hypoplasia. The patient was a 19 year-old male. Transthoraic echocardiogram and cardiac catheterization revealed a perimembranous VSD (2 cm in diameter), severe AR, annuloaortic ectasia, bipartite right ventricle with hypoplasia, and hypoplastic tricuspid valve. Operative findings showed that free margins of the right and noncoronary cusps were markedly elongated, thickened, and retracted, and commissure between the right coronary cusp and the noncoronary cusp was fused and calcified. VSD was closed with an autologous pericardial patch and composite graft aortic root replacement using direct coronary button reimplantation was performed, and the hypertrophic muscle of the right ventricular outflow tract was resected. The patient had transient weaning failure of cardiopulmonary bypass and was discharged at the postoperative 14 days without any problems.
