Bidirectional Cavopulmonary Shunt for Isolated Right Ventricular Endomyocardial Fibrosis.
- Author:
Young Jun SEO
1
;
Deok Heon LEE
;
Nam Hee PARK
;
Sae Young CHOI
;
Young Sun YOO
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Keimyung University, School of Medicine, Korea. nhpark@dsmc.or.kr
- Publication Type:Case Report
- Keywords:
Endomyocardial fibrosis;
Bidirectional cavo-pulmonary shunt;
Shunt
- MeSH:
Adult;
Cyanosis;
Dyspnea;
Echocardiography;
Endomyocardial Fibrosis*;
Follow-Up Studies;
Fontan Procedure*;
Heart Atria;
Heart Septal Defects, Atrial;
Humans;
Postoperative Period;
Tricuspid Valve;
Tricuspid Valve Stenosis
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2003;36(7):523-526
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A 44-year-old man had been admitted for dyspnea on exertion and abdominal distension. The echocardiography revealed abnormal mass in right atrium and tricuspid valve stenosis with right ventricular obliteration. The operation was performed with mass removal, enlargement of tricuspid valve opening, and right ventricular endocardiectomy. And then, atrial septal defect was made due to inadequate right ventricular volume. The patient's symptom was improved and he discharged without events. The endomyocardial fibrosis was diagnosed with microscopic examination. Eighteen months later, the patient was readmitted due to aggravated dyspnea and cyanosis. The right ventricular obliteration was progressed and pulmonary blood flow was severely decreased in follow up echocardiography. Palliative bidirectional cavo-pulmonary shunt was performed due to functional single ventricle. The dyspnea and cyanosis was markedly improved. Bidirectional cavo-pulmonary shunt for advanced and isolated right ventricular endomyocardial fibrosis provided effective palliation at early postoperative period, However, long-term follow up is mandatory.
