Pulmonary Artery Sarcoma: One Case Report.
- Author:
Hyeong Ryul KIM
1
;
Kyung Hwan KIM
;
Hyuk AHN
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital Seoul National University, College of Medicine, Korea. ahnhyuk@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Pulmonary artery;
Vascular neoplasm;
Sarcoma
- MeSH:
Adult;
Chemotherapy, Adjuvant;
Diagnosis;
Drug Therapy;
Endarterectomy;
Follow-Up Studies;
Heart Failure;
Humans;
Neoplasm Metastasis;
Neoplasm, Residual;
Pulmonary Artery*;
Rare Diseases;
Ribs;
Sarcoma*;
Thorax;
Vascular Neoplasms
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2002;35(9):692-696
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Pulmonary artery sarcoma is a rare disease and hard to diagnose; therefore, suspicion is very important for the diagnosis and treatment. Surgical resection is almost always needed because of progressive right heart failure. Adjuvant chemotherapy and radiation therapy are still controversial. We report a case of a 42-year-old man who had a right pulmonary arterial tumor. Curative resection was impossible because the tumor invaded the left pulmonary artery. Palliative endarterectomy was performed followed by radiation therapy. The patient refused the chemotherapy. Until the postoperative 6th month, the residual tumor was stable. However, 15 months later, follow-up chest computed tomography revealed a metastatic pulmonary nodule at left lower lobe and the increased residual tumor. The patient received chemotherapy with limited tumor response. The metastatic nodule and residual tumor did not increase but bone scan revealed a rib metastasis at postoperative 24 months. He will be receiving additional chemotherapy.
