Aplasia Cutis Congenita.
- Author:
Joon CHUNG
;
Won Soo LEE
;
Sung Ku AHN
- Publication Type:Case Report
- Keywords:
Aplasia Cutis Congenita
- MeSH:
Capillaries;
Connective Tissue;
Cranial Fontanelles;
Diagnosis;
Ectodermal Dysplasia*;
Epidermis;
Humans;
Infant, Newborn;
Scalp;
Skin
- From:Korean Journal of Dermatology
1994;32(4):698-702
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Aplasia cutie congenita is a rare congenital disease showing focal abscence of skin. In the msjority of instances it is limited ta the scalp especially on the vertex although other areas of the body may also be involved. Other congenital malformation have been reported to ccur with ACC odcasionally. Diagnosis depends on primarily clinical findings. The histologic finding virious from an absence of appendages to the involvement of varying layers of skin, occasionally extending to the bane or dura. Healed lesions often demonstrate a flattened epidermis, a proliferation of fibrobasts in a loose connective tissue stroma, newly formed capillaries, and a complete absence of adnexa stuctures. We observed a newborn infant with aplssia cutis congenita. The akir, defect was found on the posterior fontanelle. No associating cangenital anomalies were found in this case.
