A Case of Phakomatosis Pigmentovascularis Associated with Leg - Length Discrepancy.
- Author:
Jae Young CHOI
;
Mu Hyoung LEE
;
Choong Rim HAW
- Publication Type:Case Report
- Keywords:
Leg Length Discrepancy;
Phakomatosis Pigmentovascularis
- MeSH:
Child;
Female;
Hemangioma;
Humans;
Leg*;
Neurocutaneous Syndromes*;
Nevus;
Nevus of Ota;
Parturition;
Port-Wine Stain
- From:Korean Journal of Dermatology
1994;32(4):707-712
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Phakomatosis pigmentovascularis was first reported in 1947 as adiease complex with a distinct association of pigmentary nevus such as nevus of Ota, nevus of Ito, bilon golian spots, nevus spilus and cutaneous hemangioma such as nevus flammeus, which wss assoeisted with systemic organ involvment, We report a case of phakomatosis pigmentovascularis in a 11-year-old girl who had nevus flammeus, nevus spilus, and n.evus of Ota over various parts of her bo by since birth. She was also associated with leg-length discrepancy, but other systemic involvement was absent,