Anesthetic Management in Pediatric Patient with Prader-Willi Syndrome: A case report.
10.4097/kjae.2004.47.3.439
- Author:
Sam Hong MIN
1
;
Choon Hak LIM
;
Hye Won LEE
;
Hae Ja LIM
;
Suk Min YOON
;
Seong Ho CHANG
Author Information
1. Department of Anesthesiology and Pain Medicine, College of Medicine, Korea University, Seoul, Korea. torchid@korea.ac.kr
- Publication Type:Case Report
- Keywords:
anesthetic management;
Prader Willi syndrome
- MeSH:
Child;
Chromosome Aberrations;
Communicable Diseases;
Humans;
Intellectual Disability;
Muscle Hypotonia;
Obesity, Morbid;
Prader-Willi Syndrome*;
Scoliosis;
Sleep Apnea Syndromes;
Strabismus
- From:Korean Journal of Anesthesiology
2004;47(3):439-441
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Prader-Willi syndrome is brought by chromosomal abnormality and is characterized by mental retardation, morbid obesity, infantile hypotonia, hypogenitalism. While feeding problems arise during infancy due to hypotonia, it is followed by hyperphasia that is prone to morbid obesity leading to cardiovascular problems, diabetes, and infectious diseases. And sleep apnea, scoliosis make anesthetic management difficult. We report a case of general anesthetic management during strabismus surgery in a child with Prader-Willi syndrome and its possible considerations.
