Platypnea-Orthodeoxia Syndrome Two Decades after Definitive Surgical Repair of Pulmonary Atresia with Intact Ventricular Septum.
10.3349/ymj.2016.57.3.799
- Author:
Meng Luen LEE
1
;
Ing Sh CHIU
Author Information
1. Department of Pediatrics, Division of Pediatric Cardiology, Changhua Christian Children's Hospital, Changhua, Taiwan. ferdielee@yahoo.com
- Publication Type:Case Reports
- Keywords:
Clubbing fingers;
platypnea-orthodeoxia syndrome;
secundum atrial septal defect;
Amplatzer Septal Occluder
- MeSH:
Dyspnea/*diagnosis/*etiology/surgery;
Female;
Heart Defects, Congenital/complications/*surgery;
Heart Septal Defects, Atrial/*complications/*diagnosis/surgery;
Humans;
Hypoxia;
Pulmonary Atresia/complications/*surgery;
*Septal Occluder Device;
Syndrome;
Treatment Outcome
- From:Yonsei Medical Journal
2016;57(3):799-802
- CountryRepublic of Korea
- Language:English
-
Abstract:
A 20-year-old female had undergone definitive surgical repair for pulmonary atresia with intact ventricular septum soon after birth. She was referred to our institution with the chief complaint of clubbing fingers. A thorough examination revealed platypnea-orthodeoxia syndrome due to an interatrial right-to-left shunt through a secundum atrial septal defect. Percutaneous closure with an Amplatzer Septal Occluder resulted in resolution of the syndrome.
