A Case Report of Systemic Mastocytosis.
- Author:
Kwang Tae CHUNG
1
;
Jahoon KOO
;
Sae Kwang MOON
Author Information
1. Department of pediatrics, Kyung Pook National University, School of Medicine, Taegu, Korea.
- Publication Type:Original Article
- MeSH:
Abdominal Pain;
Biopsy;
Child;
Constipation;
Humans;
Intestine, Small;
Liver;
Male;
Mast Cells;
Mastocytosis, Systemic*;
Parturition;
Physical Examination;
Pruritus;
Sensation;
Skin;
Spleen;
Vital Signs
- From:Journal of the Korean Pediatric Society
1979;22(7):546-549
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A case of systemic mastocytosis in a 6 year old boy was presented. Skin lesions started to appear and spred several days after birth along with severe itching sensation, and intermitent abdominal pain & constipation developed at the age of 5. On physical examination, he was found to be underdeveloped (Height less than 3rd percentile) with normal vital signs. Liver was felt 1 1/2 fb below costal margin, spleen 2 fb. There were many brown to dark brown-colored irregular shaped maculopapulourticarial skin lesions, scattered all over the body, along with multiple thickened areas, and positive Darier's sign was noted. On upper GI series, many honey-combed filling defect were found throughout small intestine. Skin biopsy confirmed the diagnossis : showing multiple scattered infilteration of mast cells.
