A Pediatric Case of Primary Sjogren's Syndrome Associated with Nephrogenic Diabetes Insipidus and Renal Tubular Acidosis.
- Author:
Jong Won CHOI
1
;
You Jin JUNG
;
Jin Soon SUH
;
So Hyun PARK
;
Dae Kyun KOH
Author Information
1. Department of Pediatrics, The Catholic University of Korea, College of Medicine, Seoul, Korea. nicedoc@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
Sjogren's syndrome;
Diabetes insipidus;
Renal tubular acidosis;
Child
- MeSH:
Acidosis, Renal Tubular;
Adult;
Central Nervous System;
Child;
Diabetes Insipidus;
Diabetes Insipidus, Nephrogenic;
Humans;
Kidney;
Lacrimal Apparatus;
Liver;
Lung;
Pancreas;
Sjogren's Syndrome;
Skin
- From:Journal of the Korean Society of Pediatric Nephrology
2012;16(2):126-131
- CountryRepublic of Korea
- Language:English
-
Abstract:
Sjogren's syndrome (SS) is an autoimmune disorder primarily affecting the salivary and lacrimal glands. In addition, extra-glandular manifestations involving the lungs, liver, kidneys, pancreas, skin and central nervous system were reported in patients with SS. These extra-glandular manifestations are not rare in adult patient, but are very rare in pediatric SS. Renal manifestations are relatively common in adult SS, but are rarely reported in childhood SS. We experienced a girl with primary SS manifested with nephrogenic diabetes insipidus and renal tubular acidosis.
