Anesthesia for Living Related Liver Transplantation in Argininosuccinic Acidemia: A case report.
10.4097/kjae.2005.49.4.563
- Author:
So Young BAN
1
;
Bon Nyeo KOO
;
Jong Ho LEE
;
Soon Ho NAM
Author Information
1. Department of Anesthesiology and Pain Medicine, Yonsei University College of Medicine, Seoul, Korea. nsh66@yumc.yonsei.ac.kr
- Publication Type:Case Report
- Keywords:
argininosuccinic acidemia;
liver transplantation
- MeSH:
Anesthesia*;
Argininosuccinic Aciduria*;
Blood Pressure Monitors;
Body Temperature;
Catheterization;
Catheters;
Child;
Electrocardiography;
Female;
Femoral Artery;
Hepatic Artery;
Humans;
Liver Diseases;
Liver Transplantation*;
Liver*;
Reference Values;
Subclavian Vein;
Veins
- From:Korean Journal of Anesthesiology
2005;49(4):563-566
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We describe our initial experience of the perioperative anesthetic care provided to 8 years old female child with argininosuccinic acidemia undergoing living-related liver transplantation because it is the only available therapy for end-stage liver disease. Induction and maintenance of anesthesia has been conventional method. Arterial catheterized at radial and femoral arteries for continuous blood pressure monitoring and sampling. 18 G central vein catheterization was placed in left subclavian vein for fluid, drug infusion and CVP monitoring. EKG, pulse oxymetry, end-tidal CO2, urine output and body temperature were monitored. CBC, PT, aPTT, serum electrolyte were checked at preanhepatic, anhepatic phase and just after hepatic artery anastomosis. ABGA was checked every 1 hour. The level of serum ammmonia returned to normal range without protein restriction. We describe this case and a brief review of the literature.
