A Case of Atypical Miller-Fisher Syndrome with Internal Carotid Artery Stenosis.
- Author:
Ji Hoon JIN
1
;
Eun Hye CHOI
;
Sung Dae CHO
;
Byong Kwan SON
;
Sung Mo KANG
;
Young Se KWON
Author Information
1. Department of Pediatrics, College of Medicine, Inha University, Korea. ysped@inha.ac.kr
- Publication Type:Case Report
- Keywords:
Miller Fisher Syndrome;
Polyneuropathies;
Child;
Vascular stenosis
- MeSH:
Ataxia;
Brain Stem;
Carotid Artery, Internal;
Carotid Stenosis;
Child;
Encephalitis;
Gastrointestinal Diseases;
Guillain-Barre Syndrome;
Humans;
Immunoglobulin G;
Miller Fisher Syndrome;
Ophthalmoplegia;
Polyneuropathies;
Prednisolone;
Respiratory Insufficiency
- From:
Journal of the Korean Child Neurology Society
2010;18(2):311-316
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Miller-Fisher syndrome is an acute poly-neuropathy typically characterized by the triad of ophthalmoplegia, ataxia, and areflexia. Other poly-neuropathy diseases include Guillain-Barre syndrome and Bickerstaff brainstem encephalitis. However, not all cases of Miller-Fisher syndrome have the typical three symptoms. These diseases have been differentiated by clinical manifestations and anti-GQ1b IgG antibody testing. In Miller-Fisher syndrome, anti-GQ1b IgG antibody is present in over 95% of patients; however, the frequency is not so high in normal subjects or in those with other poly-neuropathy diseases. Infectious illnesses, such as respiratory diseases and gastrointestinal diseases, usually precede Miller-Fisher syndrome. In general, Miller-Fisher syndrome is a self-limiting illness; however, a few cases of Miller-Fisher syndrome progressing to respiratory failure have been reported, particularly in children. In this case, we report abnormal angiographic findings. We report a case of atypical Miller-Fisher syndrome with internal carotid artery stenosis treated with prednisolone.
