A Case of Progressive Facial Hemiatrophy.
- Author:
Chi Yeon KIM
1
;
Chee Won OH
Author Information
1. Department of Dermatology, School of Medicine, Gyeongsang National University and Gyeongsang Instiute of Health Science, Jinju, Korea. deroh@nongae.gsnu.ac.kr
- Publication Type:Case Report
- Keywords:
Progressive facial hemiatrophy;
Scleroderma en coup de sabre
- MeSH:
Atrophy;
Child;
Facial Hemiatrophy;
Humans;
Muscles;
Scleroderma, Localized;
Sclerosis;
Skin
- From:Korean Journal of Dermatology
2008;46(11):1538-1542
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Progressive facial hemiatrophy (PFH) was first described by Parry and Romberg and this is a rare disorder of an unknown origin. PFH is characterized by slowly progressive, mostly unilateral facial atrophy of the skin, soft tissues, muscles and underlying bony structures and is usually develops in the first or second decade of life. Although the clinical presentation of PFH may appear similar to localized linear scleroderma en coup the sabre, some patients presenting with PFH have neither en coup the sabre nor generalized sclerosis. Herein, we report on an unusual case of a 7-year-old girl who presented with progressive hemiatrophy of the face.