Anesthetic management of a patient with branchio-oto-renal syndrome.
10.17245/jdapm.2017.17.3.215
- Author:
Masanori TSUKAMOTO
1
;
Takeshi YOKOYAMA
Author Information
1. Department of Dental Anesthesiology, Kyushu University Hospital, Fukuoka, Japan. tsukamoto@dent.kyushu-u.ac.jp
- Publication Type:Case Report
- Keywords:
Branchio-oto-renal Syndrome;
Congenital Heart Disease;
Difficult Airway;
General Anesthesia;
Renal Failure
- MeSH:
Adolescent;
Airway Management;
Anesthesia, General;
Branchio-Oto-Renal Syndrome;
Branchioma;
Ductus Arteriosus, Patent;
Ear;
Ear, External;
Female;
Hearing Loss;
Heart Defects, Congenital;
Hemodynamics;
Humans;
Renal Insufficiency;
Retrognathia;
Tooth, Supernumerary
- From:Journal of Dental Anesthesia and Pain Medicine
2017;17(3):215-217
- CountryRepublic of Korea
- Language:English
-
Abstract:
Branchio-oto-renal syndrome (BOR) is a rare autosomal dominant disorder. The features include branchial cysts, hearing loss, ear malformation, preauricular pits, retrognathia, congenital heart disease, and renal abnormalities. However, anesthetic management of these patients has seldom been reported. We report a case in which general anesthesia was performed for dental treatment in a patient with BOR. Airway management, renal function, and hemodynamic changes can be of critical concern during anesthetic management. A 13-year-old girl diagnosed with BOR had severe right hearing loss, right external ear malformation, renal abnormalities, and postoperative patent ductus arteriosus (PDA). Dental extraction under general anesthesia was scheduled for a supernumerary tooth. The procedure was completed with sufficient urine volume, adequate airway management, and stable hemodynamics.
