A Case of Ovarian Mature Cystic Teratoma in Woman with Turner syndrome.
- Author:
Hyun Woo NAM
1
;
Jin Hee LEE
;
Yoon Sook KIM
;
Jong Soo KIM
;
Seung Do CHOI
;
Dong Han BAE
Author Information
1. Department of Obstetrics and Gynecology, College of Medicine, Soonchunhyang University, Soonchunhyang Chunan Hospital, Chunan, Korea. IM_Doc@hotmail.com
- Publication Type:Case Report
- Keywords:
Ovarian mature cystic teratoma;
Turner syndrome
- MeSH:
Dysgerminoma;
Female;
Gonadoblastoma;
Humans;
Incidence;
Live Birth;
Lymphocytes;
Mosaicism;
Parturition;
Teratoma*;
Turner Syndrome*
- From:Korean Journal of Obstetrics and Gynecology
2005;48(4):1029-1032
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Ovarian tumors in patients with Turner's syndrome are extremely rare. Turner syndrome occurs in 1 of 4000 to 10,000 live births, giving an approximate incidence of 1 to 2,500 live female births. Approximately half of the patients with Turner syndrome have "pure" 45,X cells in peripheral blood lymphocytes. Thirty to forty percents of Turner syndrome patients present mosaicism: 10-15% of the total group are 45,X/46,XX and 2 to 5% are 45,X/46,XY. In 45,X/46,XY Turner syndrome, the risk of developing a tumor is as high as 15-25%, with the possible development of dysgerminoma or gonadoblastoma. Recently, we experienced a case of a very rare left ovarian mature cystic teratoma in a 45,X/46,XX Turner syndrome, so report with a brief review of literature.