Diagnosis and Symptomatic Treatment of Early Reactive Cardiac Amyloidosis in Systemic Sclerosis.
10.4078/jrd.2015.22.2.132
- Author:
Rae Seok LEE
1
;
Hyun Jin SUNG
;
Jung Im JUNG
;
Hea Ok JUNG
;
Seung Min JUNG
;
Jennifer Jooha LEE
;
Seung Ki KWOK
;
Ji Hyeon JU
;
Sung Hwan PARK
Author Information
1. Division of Rheumatology, The Catholic University of Korea, Seoul St. Mary's Hospital, Seoul, Korea. rapark@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
Systemic scleroderma;
Restrictive cardiomyopathy;
Cardiac amyloidosis
- MeSH:
Amyloidosis*;
Cardiomyopathy, Restrictive;
Connective Tissue Diseases;
Diagnosis*;
Humans;
Scleroderma, Systemic*
- From:Journal of Rheumatic Diseases
2015;22(2):132-136
- CountryRepublic of Korea
- Language:English
-
Abstract:
Systemic sclerosis as a connective tissue disease could affect all internal organs of the body and could also manifest as a cutaneous lesion. Cardiac involvement leading to cardiac manifestations in systemic sclerosis patients is not rare. However, cardiac amyloidosis combined with systemic sclerosis is extremely rare. Although there were no definite treatment options in this case, symptomatic treatment is the cornerstone of the management plan. In this case report, we described a correct diagnosis and symptomatic medical care of early reactive cardiac amyloidosis with systemic sclerosis and summarize the current state of the relevant literature.
