A Cases of Familial Spastic Paraplegia (FSP).
- Author:
Jung Sang HA
1
;
Won Hee CHOI
;
Choong Seo PARK
;
Yung Joo BYUN
;
Bo Wan SEO
Author Information
1. Department of Neurology, Pathology, Yungnam University.
- Publication Type:Case Report
- MeSH:
Adolescent;
Age of Onset;
Amyotrophic Lateral Sclerosis;
Diagnosis, Differential;
Gait;
Humans;
Lower Extremity;
Male;
Muscle Spasticity*;
Paraplegia*;
Upper Extremity;
Wills
- From:Journal of the Korean Neurological Association
1985;3(2):291-297
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We present a family of FSP with review of literatures. Seeligmuller (1876) and Strumpell (1880) were the first to describe familial case of spastic paraplegia characterized by progressive weakness and spasticity of the lower limbs with little or no involvement of the upper extremities. This syndrome is heterogenous in inheritance, age of onset, severity and associated signs. A pure type without complications has been named "Strumpell's FSP". We have recently experienced a case of 17 years old male who had bilateral weakness and stiffness of lower extremities, and gait disturbance with family history. Differential diagnosis, particularly with familial amyotrophic lateral sclerosis, is discussed.
