A Case of Erdheim-Chester Disease Mimicking Systemic Lymphangitic Metastasis.
- Author:
Yun Su SIM
1
;
Jin Kyeong PARK
;
Jin Hwa LEE
;
Dong Eun SONG
;
Jung Hyun CHANG
Author Information
1. Department of Internal Medicine, Ewha Womans University School of Medicine, Ewha Medical Research Institute, Seoul, Korea. hs1017@ewha.ac.kr
- Publication Type:Case Report
- Keywords:
Erdheim-Chester disease;
Lung;
Retroperitoneal fibrosis
- MeSH:
Cough;
Dyspnea;
Erdheim-Chester Disease;
Female;
Histiocytosis;
Humans;
Lung;
Middle Aged;
Neoplasm Metastasis;
Retroperitoneal Fibrosis
- From:Korean Journal of Medicine
2011;80(6):712-717
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Erdheim-Chester disease (ECD) is non-Langerhans cell histiocytosis that leads to multi-organ involvement with unknown etiology. We report a 64-year-old woman with a dry cough and dyspnea. She had interlobular septal thickening and ground-glass opacity in both lungs, suggesting lymphangitic lung metastasis. However, she was diagnosed with ECD after a long bone and immunohistological evaluation.
