A Case of Extensive IgG4-Related Disease Presenting as Massive Pleural Effusion, Mediastinal Mass, and Mesenteric Lymphadenopathy in a 16-Year-Old Male.
10.4046/trd.2015.78.4.396
- Author:
Eun Kyong GOAG
1
;
Ji Eun PARK
;
Eun Hye LEE
;
Young Mok PARK
;
Chi Young KIM
;
Jung Mo LEE
;
Young Joo KIM
;
Young Sam KIM
;
Se Kyu KIM
;
Joon CHANG
;
Moo Suk PARK
;
Kyung Soo CHUNG
Author Information
1. Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. chungks@yuhs.ac
- Publication Type:Case Report
- Keywords:
Pleural Effusion;
Mediastinum
- MeSH:
Adolescent*;
Child;
Humans;
Immunoglobulin G;
Lymphatic Diseases*;
Male*;
Mediastinum;
Plasma Cells;
Pleural Effusion*
- From:Tuberculosis and Respiratory Diseases
2015;78(4):396-400
- CountryRepublic of Korea
- Language:English
-
Abstract:
IgG4-related disease is an immune-mediated fibro-inflammatory disease, characterized by lymphoplasmacytic infiltration composed of IgG4-positive plasma cells of various organs with elevated circulating levels of IgG4. This disease is now reported with increasing frequency and usually affects middle-aged men. Massive pleural effusion in children is an uncommon feature in IgG4-related disease. Here, we report a case of a 16-year-old male patient with extensive IgG4-related disease presenting with massive pleural effusion, mediastinal mass, and mesenteric lymphadenopathy.
