A Case of Primary Retroperitoneal Synovial Sarcoma.
- Author:
Bo Sung SOHN
1
;
Kee Whan KIM
;
Chang Hyeok AN
;
Jeong Soo KIM
;
Wook KIM
;
Seung Jin YOO
;
Keun Woo LIM
;
Eun Jeong LEE
;
Young Mi KU
Author Information
1. Department of Surgery, Uijongbu St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Uijeongbu, Korea. achcolo@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
Retroperitoneal neoplasm;
Synovial sarcoma
- MeSH:
Diagnosis;
Extremities;
Joints;
Mesoderm;
Mortality;
Necrosis;
Recurrence;
Retroperitoneal Neoplasms;
Retroperitoneal Space;
Sarcoma, Synovial*
- From:Journal of the Korean Surgical Society
2003;64(3):256-260
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A retroperitoneal Synovial Sarcoma is defined as a tumor arising in the retroperitoneal space, with an origin of mesodermal structures. The majority of synovial sarcomas (85 to 95%) occur in the extremities, located near the large joints. They are uncommon, and usually appear as a non- specific soft tissue mass, with no specific imaging feature. However, in some cases, radiological findings and anatomic location of the tumor may help the diagnosis. On CT examination, these tumors may be shown as hypo-dense masses and have an irregular enhancement in the periphery, with a poor enhancement in the central area, reflecting the necrotic, cystic and hemorrhagic changes. Histologically, there are two types of synovial sarcoma: biphasic and monophasic. Both types have about a 40% mortality rate. The known prognostic factors are; frequent mitotic figures, extensive tumor necrosis, and poor differentiation. Surgical ablation remains the mainstay of their management. Regardless of adequate surgical and adjunctive therapies, the recurrence rate ranges from 28 to 36%. Here, we present a case of a retroperitoneal synovial sarcoma, with a review of the literature.
