A Case of Pulmonary Artery Sling Associated with Tracheobroncheal Hypoplasia.
- Author:
Yong Han SUN
1
;
Ho Sung KIM
;
Jung Il NOH
;
Jung Yun CHOI
;
Yong Soo YUN
Author Information
1. Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Pulmonalry artery sling;
Tracheobronchial hypoplasia
- MeSH:
Angiography;
Aorta, Thoracic;
Bronchography;
Cyanosis;
Ductus Arteriosus, Patent;
Echocardiography;
Esophagus;
Female;
Heart Septal Defects, Atrial;
Heart Septal Defects, Ventricular;
Humans;
Lung;
Pulmonary Artery*;
Trachea;
Vena Cava, Superior
- From:Journal of the Korean Pediatric Society
1996;39(3):417-422
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Pulmonary artery sling is a rare vascular anomaly wherein the left pulmonary artery arises from the right pulmonary artery and then traverses between the esophagus and the trachea toward the hilum of the left lung. Associated anomalies are common, particularly those of the tracheobronchial tree, which have been found in more than 50% of patients. Cardiovascular anomalies such as persistent left superior vena cava, atrial septal defect, ventricular septal defect, patent ductus arteriosus and aortic arch anomalies are also found not infrequently. We have experienced a 20 day-old female who had showed severe respiratory distress and cyanosis. She was diagnosed as pulmonary artery sling associated with tracheobronchial hypoplasia by echocardiography, angiography, esophagography and bronchography. We report this case with related literature review.