A Case of Nonfamilial Generalized Gastrointestinal Juvenile Polyposis with Pancytopenia.
- Author:
Jong Ook KIM
1
;
Heung Pyo KONG
;
Kang Seo PARK
;
Wan Seob KIM
;
Chun Hee LEE
Author Information
1. Department of Pediatrics, Presbyterian Medical Center, Chonju, Korea.
- Publication Type:Case Report
- Keywords:
Juvenile poluposis;
GI tract;
Pancytopenia
- MeSH:
Adolescent;
Anemia;
Anemia, Iron-Deficiency;
Child;
Colectomy;
Gastrointestinal Neoplasms;
Gastrointestinal Tract;
Hemorrhage;
Humans;
Male;
Pancytopenia*;
Polyps
- From:Journal of the Korean Pediatric Society
1996;39(3):423-430
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
In contrast to the child with a solitary juvenile polyp, generalized gastrointestinal juvenile polyposis have a much different clinical course. In generalized juvenile polyposis blood loss can be considerable and iron-deficiency anemia is a common observation. Although it is usually regarded as a benign condition, juvenile polyposis may predispose to cancer of the gastrointestinal tract. We experienced a case of nonfamilial generalized gastrointestinal juvenile polyposis with pancytopenia in a 15 year-old male patient who had hospitalized because of intermittent rectal bleeding with anemia for three years. Histological examination of polyps from affected patient revealed a spectrum of change from juvenile polyps, to juvenile polyps with adenomatous changes. Subtotal colectomy, rectal mucosectomy, and endorectal pull-through procedure were successfully performed. No complication has occured since the discharge. A brief review of related literatures is also presented.
