Perivascular Epithelioid Cell Tumor (PEComa) of Abdominal Cavity from Falciform Ligament: A Case Report.
10.3346/jkms.2009.24.2.346
- Author:
Cheol Woong CHOI
1
;
Tae Oh KIM
;
Kyung Yeob KIM
;
Sun Mi LEE
;
Gwang Ha KIM
;
Dae Hwan KANG
;
Geun Am SONG
;
Suk KIM
;
Dae Hwan KIM
Author Information
1. Department of Internal Medicine, Pusan National University College of Medicine, Busan, Korea.
- Publication Type:Case Report
- Keywords:
Angiomyolipoma;
Perivascular Epithelioid Cell Neoplasms;
Lymphangiomyomatosis;
Perivascular Epithelioid Cell Neoplasms
- MeSH:
Abdominal Neoplasms/*diagnosis/pathology/surgery;
Actins/metabolism;
Adult;
Antigens, Neoplasm/metabolism;
Humans;
*Ligaments/pathology;
Male;
Neoplasm Proteins/metabolism;
Perivascular Epithelioid Cell Neoplasms/*diagnosis/pathology/surgery;
S100 Proteins/metabolism;
Tomography, X-Ray Computed
- From:Journal of Korean Medical Science
2009;24(2):346-349
- CountryRepublic of Korea
- Language:English
-
Abstract:
We present a case of perivascular epithelioid cell tumors (PEComas) in the abdominal cavity at the falciform ligament. A 30-yr-old Korean man visited to hospital for the evaluation of a growing, palpable abdominal mass. He had felt the mass growing over 6 months. There was no family or personal history of tuberous sclerosis. The resected specimen showed a mass of 8.0x7.0x5.5 cm in size. Histological examination showed sheets of spindle-to-epithelioid cells with clear-to-eosinophilic cytoplasm. Immunohistochemically, tumor cells were positive for HMB-4 (gp100) and smooth muscle actin. They were also positive for the S-100, which is a marker of neurogenic and melanocytic tumors. Patient was treated with radical resection of tumor without any adjuvant therapy. He is well and on follow-up visits without tumor recurrence.
