A Case of Simple Type Caroli's Disease Confined to Right Lobe of the Liver.
- Author:
Ho KIL
1
;
Eun Young CHOI
;
Jee In JEONG
;
Chan Sun PARK
;
Seon Mee PARK
;
Seok Hyung KIM
;
Kil Sun PARK
;
Lee Chan JANG
Author Information
1. Department of Internal Medicine, Chungbuk National University College of Medicine, Cheongju, Korea. smpark@chungbuk.ac.kr
- Publication Type:Case Report ; English Abstract
- Keywords:
Caroli's disease;
Monolobar type;
Right hepatic lobectomy
- MeSH:
Adult;
Bile Ducts, Intrahepatic/pathology;
Caroli Disease/diagnosis/pathology/*surgery;
Common Bile Duct/surgery;
Diagnosis, Differential;
Hepatectomy;
Humans;
Liver/*pathology;
Magnetic Resonance Imaging;
Male;
Tomography, X-Ray Computed
- From:The Korean Journal of Gastroenterology
2007;50(4):271-276
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Caroli's disease is a rare congenital hepatobiliary disease characterized by multifocal segmental dilatation of intrahepatic bile ducts affecting all or parts of the liver. Two forms of Caroli's disease are described, the pure form and that associated with periportal fibrosis. The disease may diffusely affect the liver or be localized to one lobe or segment. Less than 20% of all reported cases of Caroli's disease are monolobar type. We report a case of simple type Caroli's disease confined to right lobe of the liver in a 22 year old man. He was admitted due to right upper abdominal pain and diagnosed by magnetic resonance cholangiopancreatography. He was treated with right hepatic lobectomy and recovered completely.
