Surgical Treatment of Ebstein Anomaly: One Case Report.
10.4070/kcj.1976.6.2.25
- Author:
Yo Jun SONG
;
Nam Soo LEE
;
Hyoung Mook KIM
- Publication Type:Case Report
- MeSH:
Anoxia;
Autopsy;
Brain;
Cause of Death;
Child;
Death, Sudden, Cardiac;
Diagnosis;
Dilatation;
Ebstein Anomaly*;
Edema;
Female;
Heart;
Heart Atria;
Heart Ventricles;
Hemorrhage;
Humans;
Korea;
Liver;
Lung;
Myocardium;
Palliative Care;
Pulmonary Artery;
Pulmonary Atelectasis;
Thoracic Surgery;
Thoracic Wall;
Tuberculosis
- From:Korean Circulation Journal
1976;6(2):25-31
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
In the Dept. of Thoracic Surgery, Korea University Hospital, Preoperative diagnosis as Ebstein anomaly was made on the 11-year old female through the preoperative examination including right cardioangiography and the Glenn Operation was performed to this patients as palliative treatment. During closure of the thoracic wall just after the anastomosis of S.V.C. and right pulmonary artery, sudden cardiac arrest developed. One day later after death, autopsy was performed in order to confirm the pathologic anatomy of the cardiac anomaly and to clarify the cause of death. Pathologic anatomy of the heart revealed the huge dilatation of right atrium, Patent Foramin Ovale, and the deformed and descended posterior and the septal leaflets of tricuspid value by which right ventricle was devided into the atrialized and the functional portion. The diagnosis of the autopsy showed (1) Ebstein Anomaly (2) bilateral total atelectasis of the lung, (3) multiple petechial hemorrhage and edema of the myocardium, brain and liver due to acute hypoxia, (4) fibrocaseous tuberculosis of the liver and tuberculous pericholangitis.
