A case of systemic lupus erythematosus with chylothorax, chronic interstitial cystitis and protein-losing enteropathy.
- Author:
Kung No LEE
1
;
Young Hwan PARK
;
Seung Hwan LEE
;
Jae Chun LEE
;
Mi Kyoung LIM
;
You Sook CHO
;
Bin YOU
;
Hee Bom MOON
Author Information
1. Department of Internal Medicine, Asan Medical Center University of Ulsan College of Medicine, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Lupus erythematosus;
Systemic;
Cystitis, Interstitial;
Protein-losing enteropathy
- MeSH:
Chylothorax*;
Cyclophosphamide;
Cystitis, Interstitial*;
Female;
Humans;
Immune Complex Diseases;
Lupus Erythematosus, Systemic*;
Protein-Losing Enteropathies*
- From:Korean Journal of Medicine
2000;59(5):555-560
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Systemic lupus erythematosus(SLE) is the prototypic immune complex disease which involves various organs. Chronic interstitial cystitis and protein-losing enteropathy are uncommon manifestations of SLE and have good response to steroid. Only one case of SLE associated with chronic interstitial cystitis and protein-losing enteropathy has been reported which was resistant to steroid treatment but dramatically responded to cyclophosphamide. We describe a case of a female patient who developed systemic lupus erythematosus associated with chylothorax, interstitial cystitis and protein-losing enteropathy with literature review. This case was initially resistant to steroid but with the addition of cyclophosphamide, chylothorax, chronic interstitial cystitis and protein-losing enteropathy markedly improved. This is the first case of SLE that developed chylothorax as well as chronic interstitial cystitis and protein-losing enteropathy.