Right Ventricle Exclusion in Severe Neonatal Ebstein's Anomaly.
- Author:
Sun Kyung MIN
1
;
Woong Han KIM
;
Young Ok LEE
;
Yong Won SEONG
;
Sung Joon PARK
;
Jin Ho CHOI
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Seoul Paik Hospital, Inje University School of Medicine, Korea.
- Publication Type:Case Report
- Keywords:
Right ventricle;
Congenital heart disease;
Ebstein's anomaly
- MeSH:
Blalock-Taussig Procedure;
Cyanosis;
Ductus Arteriosus, Patent;
Ebstein Anomaly;
Fontan Procedure;
Heart Atria;
Heart Murmurs;
Heart Ventricles;
Humans;
Pulmonary Atresia;
Pulmonary Circulation
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2010;43(5):518-521
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A one-day-old baby was transferred for cyanosis and heart murmur. Echocardiographic evaluation revealed that he had severe neonatal Ebstein's anomaly (Carpentier type C), pulmonary atresia, and pulmonary circulation via patent ductus arteriosus. Because the wall of the atrialized right ventricle was very thin, showed decreased contractility, and the small right ventricle showed pulmonary atresia, we decided that a two-ventricular repair was impossible. When the patient was one-month-old, he underwent right atrium reduction-plasty, a right ventricular exclusion procedure (including atrialized right ventricle resection and functional right ventricle plication), and right modified Blalock-Taussig shunt. He was discharged without specific problems. He received a bidirectional cavopulmonary shunt successfully at 4 months later.
