A Case of Systemic Lupus Erythematosus with Degos' Disease.
10.4078/jkra.2007.14.3.256
- Author:
Jung Hwa LEE
1
;
Hee Jung RYU
;
Young Bae PARK
;
Byoung Yong CHOI
;
Eun Young LEE
;
Yun Jong LEE
;
Eun Bong LEE
;
Yeong Wook SONG
Author Information
1. Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea. ysong@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Malignant atrophic papulosis;
Degos' disease;
Systemic lupus erythematosus;
Antiphospholipid antibody
- MeSH:
Antibodies, Antiphospholipid;
Central Nervous System;
Erythema;
Gastrointestinal Tract;
Intestine, Small;
Kidney;
Lupus Erythematosus, Systemic*;
Malignant Atrophic Papulosis;
Pathology;
Rare Diseases;
Skin;
Viscera
- From:The Journal of the Korean Rheumatism Association
2007;14(3):256-262
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Degos' disease, malignant atrophic papulosis, is a rare disease characterized by a pathognomonic appearance of porcelain-white, atrophic papules with peripheral erythema and multiple occlusive thrombotic vascular pathology. It sometimes involves internal viscera such as the gastrointestinal tract, the central nervous system and kidney which may bring to death. Although several reports showed the associations between Degos' disease and antiphospholipid antibody or systemic lupus erythematosus, its pathogenetic significance remains elusive. The previous 4 Korean cases of Degos's disease involved only skin and/or the gastrointestinal tract. We report a case of systemic lupus erythematosus with Degos' disease involving skin, kidney and small intestine.
