A Case of Multiple Plexiform Schwannomas.
10.5021/ad.2000.12.2.130
- Author:
Joo Hyun SHIM
;
Tae Jong CHUN
;
Myeung Nam KIM
;
Kye Yong SONG
;
Byung In RO
- Publication Type:Original Article
- Keywords:
Multiple cutaneous plexiform schwannomas
- MeSH:
Child;
Christianity;
Dermis;
Humans;
Neurilemmoma*;
Neurofibroma, Plexiform;
Neurofibromatosis 1;
Peripheral Nerves;
Subcutaneous Tissue
- From:Annals of Dermatology
2000;12(2):130-133
- CountryRepublic of Korea
- Language:English
-
Abstract:
Plexiform schwannoma is a relatively rare, benign peripheral nerve sheath tumor that can be located either in the deep soft tissues or in the dermis or subcutaneous tissue. This tumor may occur singly or as multiple lesions and may be localized to one anatomic site or diffusely distributed. Plexiform schwannoma should be differentiated with plexiform neurofibroma or other plexiform malignant tumors. We describe a case of a 6-year-old patient with multiple cutaneous plexiform schwannomas who had no other stigmata of neurofibromatosis 1 or family history suggesting a genetic disorder. The histopathological study revealed a tumor composed of multiple intradermal or subcutaneous interlacing and interconnecting fascicles and nodules that vary in size and shape. Characteristic Antoni A type cellular tissue showing frequent nuclear palisading and Verocay bodies were observed within well circumscribed elongated nodules.
