A Case of Segmental Neurofibromatosis.
- Author:
Tae Kyung LEE
;
Doo Chan MOON
;
Kyung Sool KWON
;
Tae Ahn CHUNG
- Publication Type:Case Report
- Keywords:
Neurofibromas;
Segmental
- MeSH:
Biopsy;
Cafe-au-Lait Spots;
Collagen;
Female;
Humans;
Middle Aged;
Neck;
Neurofibroma;
Neurofibromatoses*;
Neurofibromatosis 1;
Shoulder
- From:Korean Journal of Dermatology
1987;25(5):696-699
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A 61-year-old female had neurofibromas situated on the right side of upper trunk, shoulder and neck in the distribution of dermatomes C3 and C4(right), which developed 3 years ago. There were not cafe-au-lait spots, axillary frecklings, or Lisch nodule (iris pignented hamartoma). Biopsy specimen showed collagenous wavy fibrils among which spindle-shaped and round cells were embedded as seen in the typical neurofibroma. This case was considered to be a segmental form of von Recklinghausen's disease.
