Churg-Strauss Syndrome Presented With Hearing Impairment and Facial Palsy.
10.5535/arm.2014.38.6.852
- Author:
Jeong Hyun BYUN
1
;
Jong Hoo LEE
;
In Sung CHOI
Author Information
1. Department of Physical & Rehabilitation Medicine, Regional Cardiocerebrovascular Center, Chonnam National University Hospital, Chonnam National University Medical School, Gwangju, Korea. drchoiis@hanmail.net
- Publication Type:Case Report
- Keywords:
Churg-Strauss syndrome;
Facial paralysis;
Hearing loss
- MeSH:
Azathioprine;
Biopsy;
Blood Vessels;
Churg-Strauss Syndrome*;
Cranial Nerves;
Eosinophils;
Facial Paralysis*;
Female;
Hearing;
Hearing Loss*;
Humans;
Middle Aged;
Prognosis;
Pulmonary Eosinophilia;
Sinusitis;
Steroids;
Tomography, X-Ray Computed;
Turbinates;
Vasculitis
- From:Annals of Rehabilitation Medicine
2014;38(6):852-855
- CountryRepublic of Korea
- Language:English
-
Abstract:
Churg-Strauss syndrome (CSS) is a rare systemic necrotizing vasculitis. Cranial nerve involvement is very rare in CSS. A 59-year-old woman had complained of both hearing impairments for eight months and left facial palsy for three months. Left facial and cochlear neuropathies were detected in electrodiagnostic studies. Paranasal sinus computed tomography (CT) showed chronic pansinusitis. Chest CT revealed eosinophilic infiltration in the right upper lobe. Tissue biopsy of the right inferior turbinate displayed necrotizing vasculitis with eosinophilic infiltration. She was diagnosed as CSS, based on the presence of eosinophilia, pulmonary infiltration, paranasal sinusitis, and biopsy containing blood vessels with extravascular eosinophils. She was treated with intravenous and oral steroids and azathioprine, showing relatively good prognosis on facial palsy and hearing impairment. We report a very rare case of CSS presented with hearing impairment and facial palsy.
