Solitary Malignant Gastrointestinal Stromal Tumor Associated with a Neurofibromatosis Type I.
10.5021/ad.2003.15.1.14
- Author:
Hyun Jin MO
;
Hyung Ok KIM
;
Chung Won KIM
;
Tae Yoon KIM
- Publication Type:Case Report
- Keywords:
Neurofibromatosis Type I;
Gastrointestinal Stromal Tumor
- MeSH:
Dermatology;
Female;
Gastrointestinal Stromal Tumors*;
Gastrointestinal Tract;
Humans;
Korea;
Middle Aged;
Neurofibromatoses*;
Neurofibromatosis 1*;
Seoul
- From:Annals of Dermatology
2003;15(1):12-14
- CountryRepublic of Korea
- Language:English
-
Abstract:
From the Department of Dermatology, College of Medicine, The Catholic University of Korea, Kangnam St. Mary's Hospital, 505, Banpo-Dong, Seocho-Gu, 137-040, Seoul, Korea, Gastrointestinal stromal tumors are usually late manifestations of neurofibromatosis (von Recklinghausen's disease) and most become clinically apparent in middle-aged patients as multiple benign tumors. To our review of the literature, solitary malignant stromal tumor of gastrointestinal tract is exceptionally rare in von Recklinghausen's disease. We herein present a case of solitary jejunal stromal tumor in a 50-year-old woman with NF1, which histopathologically showed a malignant change and combined smooth muscle-neural type.
