Pulmonary Features of Hyperimmunoglobulin E (Job's)syndrome.
10.4046/trd.2002.52.6.651
- Author:
Byoung Ju MIN
1
;
Jea Seung SHIN
;
In Sung LEE
;
Young Kyoo SHIN
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Korea University College of Medicine, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Immunologic diseases;
Immunologic deficiency syndromes;
Phagocyte bactericidal dysfunction;
Hyperimmunoglobulin E-recurrent infection syndrome;
Job's syndrome
- MeSH:
Anti-Bacterial Agents;
Empyema;
Immune System Diseases;
Immunoglobulin E;
Immunoglobulins;
Immunologic Deficiency Syndromes;
Job Syndrome;
Lung Abscess;
Phagocyte Bactericidal Dysfunction;
Pneumonia;
Pneumothorax;
Skin
- From:Tuberculosis and Respiratory Diseases
2002;52(6):651-656
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Hyperimmunoglobulin E syndrome, otherwise known as Job's syndrome, is an immune disorder characterized by an abnormal elevation of the circulating immunoglobulin E level, and recurrent infections of the skin and sinopulmo nar tract. The syndrome has various ppulmonary featurea, e.g., pneumonia, pneumatocele, pneumothorax, lung abscesses and empyema. We report a case of hyperimmunoglobulin E syndrome, with various respiratory clinical manifestation. Medical therapy, including prophylactic antibiotics, has been the cornerstone for the treatment of hyperimmunoglobulin E syndrome. Even if surgical intervention is required, minimal pulmonary parenchymal resection is recommended.
