Airway Management in a Patient with Goldenhar's Syndrome: A case report.
10.4097/kjae.2007.53.4.535
- Author:
Won Kook LEE
1
;
Eun Ju KIM
;
Ji Hyang LEE
;
Sang Gon LEE
;
Jong Suk BAN
;
Byung Woo MIN
Author Information
1. Department of Anesthesiology and Pain Medicine, Fatima Hospital, Daegu, Korea. kej1127@fatima.or.kr
- Publication Type:Case Report
- Keywords:
Goldenhar's syndrome;
propofol;
remifentanil
- MeSH:
Airway Management*;
Female;
Goldenhar Syndrome;
Humans;
Infant;
Intubation;
Propofol
- From:Korean Journal of Anesthesiology
2007;53(4):535-538
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Goldenhar's syndrome is a rare form of a hemifacial microsomia in which the facial and vertebral anomalies are frequently associated with cardiac, pulmonary and renal defects. Infants with Goldenhar's syndrome commonly have an airway that is difficulty to manage. A difficult tracheal intubation may be due to a combination of mandibular hypoplasia, macrognathia, palatal defects and vertebral anomalies. We report the successful anesthetic management of a 10-month-old girl with Goldenhar's syndrome for the excision of conjunctival lipodermoid. The use of remifentanil followed with an anesthetic induction dose of propofol provides adequate conditions for tracheal intubation without the use of neuromuscluar blocking agents in a patient with Goldenhar's syndrome.
