Juvenile Dermatomyositis Presenting as Deep Skin Ulcerations as an Initial Manifestation.
- Author:
Sun Yong KWON
1
;
Jin Kyung CHAE
;
Sang Hyun PARK
;
Joo Yeon KO
;
Seok Don PARK
;
Kun PARK
Author Information
1. Department of Dermatology, Wonkwang University School of Medicine, Korea. derma@chol.com
- Publication Type:Case Report
- Keywords:
Juvenile dermatomyositis;
Skin ulceration
- MeSH:
Arm;
Biopsy;
Child;
Dermatomyositis*;
Head;
Humans;
Male;
Muscle Weakness;
Muscle, Skeletal;
Muscular Diseases;
Myositis;
Skin Ulcer*;
Ulcer;
Vasculitis
- From:Korean Journal of Dermatology
2014;52(3):169-172
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Juvenile dermatomyositis is a common idiopathic inflammatory myopathy in childhood and is characterized by symmetric proximal muscle weakness and specific cutaneous manifestations. We here report on a 12-year-old boy who presented with violaceous maculopatches with multiple deep skin ulcerations on the right arm and lower back 4 months ago. One month after the initial visit, he had difficulty climbing stairs and elevating his arms above the head. Laboratory tests showed elevation of the serum levels of skeletal muscle enzymes, and electromyogram and muscle biopsy indicated myopathy. Histopathological analysis of the ulceration indicated necrotizing vasculitis and calcification. Based on these findings, his condition was diagnosed as juvenile dermatomyositis. We believe that this case is unique because of the difficulty in diagnosing the condition, as skin ulceration is a rare cutaneous manifestation of dermatomyositis.