A Case of Idiopathic Sclerosing Mesenteritis with Retroperitoneal Fibrosis.
10.4166/kjg.2011.58.4.221
- Author:
June Ho BAE
1
;
Seong Hwan KIM
;
Sang Bong AHN
;
Byoung Kwan SON
;
Yun Ju JO
;
Young Sook PARK
;
Yu Min JUNG
;
Yeon Soo CHANG
Author Information
1. Department of Internal Medicine, Eulji General Hospital, Eulji University College of Medicine, Seoul, Korea. shkim@eulji.ac.kr
- Publication Type:Case Reports ; English Abstract
- Keywords:
Sclerosing mesenteritis;
Retroperitoneal fibrosis;
Tamoxifen
- MeSH:
Anti-Inflammatory Agents/therapeutic use;
Antineoplastic Agents, Hormonal/therapeutic use;
Diagnosis, Differential;
Humans;
Laparoscopy;
Male;
Middle Aged;
Panniculitis, Peritoneal/complications/*diagnosis/drug therapy;
Prednisolone/therapeutic use;
Retroperitoneal Fibrosis/complications/*diagnosis/pathology;
Tamoxifen/therapeutic use;
Tomography, X-Ray Computed
- From:The Korean Journal of Gastroenterology
2011;58(4):221-225
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Sclerosing mesenteritis is a rare inflammatory disease of the bowel mesentery. It produces tumor-like masses of the mesentery composed of varying degrees of fibrosis, chronic inflammation, and fat necrosis. It has been described variously as fibrosing mesenteritis, retractile mesenteritis, mesenteric Weber Christian disease, and systemic nodular panniculitis. The etiology and pathogenesis of the disease are as yet unknown, but autoimmune disorder, previous abdominal surgery, trauma, and ischemia could play a role. The clinical features include abdominal pain, vomiting, diarrhea, and constipation. Occasionally, patients with this condition may present with bowel obstruction. Rarely, It can be associated with other idiopathic inflammatory disorders such as retroperitoneal fibrosis, sclerosing cholangitis, and orbital pseudotumors. We report a case of idiopathic sclerosing mesenteritis with retroperitoneal fibrosis in a 58-year-old man.
